Disease,Hirschsprung

《英文msh詞典》Disease,Hirschsprung
[入口詞] Disease,Hirschsprung
[主題詞] Hirschsprung Disease
[英文釋義] Congenital MEGACOLON resulting from the absence of ganglion cells (aganglionosis) in a distal segment of the LARGE INTESTINE. The aganglionic segment is permanently contracted thus causing dilatation proximal to it. In most cases,the aganglionic segment is within the RECTUM and SIGMOID COLON.

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