Triphosphate,Thiamin

《英文msh詞典》Triphosphate,Thiamin
[入口詞] Triphosphate,Thiamin
[主題詞] Thiamine Triphosphate
[英文釋義] 3-((4-Amino-2-methyl-5-pyrimidinyl)methyl)-4-methyl-5-(4,6,8,8-tetrahydroxy-3,5,7-trioxa-4,6,8-triphosphaoct-1-yl)thiazolium hydroxide,inner salt,P,P',P''-trioxide. The triphosphate ester of thiamine. In Leigh's disease,this compound is present in decreased amounts in the brain due to a metabolic block in its formation.