4-Hydroxylase,Phenylalanine
《英文msh詞典》4-Hydroxylase,Phenylalanine
[入口詞] 4-Hydroxylase,Phenylalanine
[主題詞] Phenylalanine Hydroxylase
[英文釋義] An enzyme of the oxidoreductase class that catalyzes the formation of L-TYROSINE,dihydrobiopterin,and water from L-PHENYLALANINE,tetrahydrobiopterin,and oxygen. Deficiency of this enzyme may cause PHENYLKETONURIAS and PHENYLKETONURIA,MATERNAL. EC 1.14.16.1.