Ceramides,Lactosyl

《英文msh詞典》Ceramides,Lactosyl
[入口詞] Ceramides,Lactosyl
[主題詞] Lactosylceramides
[英文釋義] Glycosphingolipids which contain as their polar head group a lactose moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue,due to a defect in lactosylceramide beta-galactosidase,is the cause of lactosylceramidosis.